ตารางที่ 5
แสดง ALPHA THALASSEMIA

Syndrome
Genotype
Clinical Feature
Hb Pattern
 New born
After 1st year
Hydrops fetalis
-- / --
Fetal or neonatal death
with severe anemia
Hb Bart's>80%
Hb H,Hb Portland
-
Hb H disease
-- / -a
(-- / aacs)
Chronic hemolytic
    anemia
Hb Bart's 20-40% 
(Hb CS present)
Hb H 5-30%
Hb Bart's+trace
(Hb CS 2-3%)
Thalassemia
   minor
-- / aa
-a / -a
Little or no anemia;
    thalassemic Rbc
Hb Bart's 2-10% None
Silent carrier
-a / aa
aa / aacs
No clinical or hemolytic
    abnormality
Hb Bart's 1-2%
(Hb CS present)
None
(Hb CS 1%)
Normal
aa / aa
No clinical or hemolytic
    abnormality
Hb Bart's 0-trace% None